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Published: 2026-07-31
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Issue
Vol. 19 No. 3 (2026)
Section
Báo cáo ca bệnh

ROUND CELL SARCOMA WITH BCOR ALTERATION: A RARE CASE REPORT AND LITERATURE REVIEW

Thach Hoang Ngoc1, Lan Bui Ngoc1, Quynh Nguyen Trong2
1 Vietnam National Children’s Hospital
2 Saint Paul Hospital

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Abstract

Round cell sarcoma with BCOR (SBCOR) alteration is a new cancer presented in the WHO classfication of tumours of soft tissue and bone. Diagnosis can base on histopathology and Immunohistochemistry (IHC) staining for BCOR. We report a case of a soft tissue and scapular tumour in a 29-month-old boy, who was diagnosed base on the feature of a round and spindle cell tumour with IHC staining positive for BCOR. The child was treated with chemotherapy combined with surgery, currently, treatment achieved a good response with no signs of recurrence. After 4 years finish of chemotherapy, the kid can perform fine motor movements of the forearm and hand.

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Keywords

BCOR

References

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