CONGENITAL INTESTINAL LYMPHANGIECTASIA CASE REPORT AT THANH HOA CHILDREN’S HOSPITAL
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Abstract
Primary intestinal lymphangiectasia is a rare condition, characterized by increased intestinal protein loss,clinical manifestation of edema, moderate diarrhea, hypoproteinemia, lymphopenia, malabsorption of vitamins and fat, dilated lymphatic vessels in the small intestine. The case reported was the fi rst PIL at Thanh Hoa Children’s Hospital. The diagnosis was confi rmed with colonoscopy and pathology results, patient was treated with albumin infusion, a fat-reducing diet and medium-chain triglyceride supplementation in combination with octretide.
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References
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with octreotide. J Gastroenterol 2001, 36: 129-132. PubMed Abstract | Publisher Full Tex.
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Rare Dis 2008, 3: 5. PubMed Abstract | BioMed Central Full Text | PubMed Central Full Text.
2. Đặng Thuý Hà, Bùi Thu Hương, Nguyễn Văn Ngoan và cs: Báo cáo ca bệnh “Giãn mạch
lympho ở ruột tiên phát được chẩn đoán bằng sinh thiết ruột non và điều trị bằng triglycerides
chuỗi trung và Octreotid”. 2013. http://benhviennhitrunguong.org.vn/thong-bao-ca-benh.html.
3. N Suresh, R Ganesh et cs: Primary intestinal Lymphangiectasia: Case report. India pediatrics
2009; 46:903-906.
4. Waldmann TA, Steinfeld JL, Dutcher TF, Davidson JD, Gordon RS: The role of the
gastrointestinal system in “idiopathic hypoproteinmia”. Gastroenterology 1961; 41: 197-207.
5. Ballinger AB,Farthing MJ: Octreotidein the treatment of intestinal lymphangiectasia. Eur J
Gastroenterol Hepatol 1998; 10: 699-702.
6. Heresbach D, Raoul JL, Genetet N et al. Immunological study in primary intestinal
lymphangiectasia. Digestion 1994; 55: 59-64
7. Mistilis SP, Stephen DD, Skyring AP: Intestinal lymphangiectasia. Mechanism of enteric loss of plasma-protein and fat.Lancet 1965, 1:77-81. PubMed Abstract .
8. Kuroiwa G, Takayama T, Sato Y et al: Primary intestinal lymphangiectasia successfully treated
with octreotide. J Gastroenterol 2001, 36: 129-132. PubMed Abstract | Publisher Full Tex.
9. Mine K, Matsubayashi S, Nakai Y, Nakagawa T: Intestinal lymphangiectasia markedly improved with antiplasmin therapy. Gastroenterology 1989, 96:1596-1599. PubMed Abstract.
10. Chen CP, Chao Y, Li CP et al: Surgical resection of duodenal lymphangiectasia: a case
report. World J Gastroenterol 2003; 9: 2880-2882.