A RARE CASE OF BRONCHIAL MUCOEPIDERMOID CARCINOMA IN PEDIATRICS

Dang Mai Lien1, Le Thanh Chuong1, Nguyen Dang Quyet1, Ton Thi Thuy Trang1, Nguyen Hoai Anh1, Bui Ngoc Lan1, Nguyen Van Linh1
1 Viet Nam National Children's Hospital

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Abstract

Mucoepidermoid carcinoma (MEC) is a common neoplasia of the salivary glands, initially described by Stewart et al. in 1945 [1]. It was reported for the first time in bronchi by Smetana et al. in 1952, and since then a few cases have been further described, given his relative rarity [2].


The precise nature of these neoplasms is not yet clear and little is known on the histogenesis and pathogenesis of the disease. This is probably due to its rarity and the small number of studies published, focusing on its molecular aspects. Here we report a case of a bronchial mucoepidermoid tumor with initial symptoms of persistent cough and lung collapse. We would like to emphasize the importance of thoroughly screening clinical and paraclinical symptoms in cases of prolonged pneumonia to identify the underlying cause of the disease.

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References

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