SURGICAL RESULT FOR REPAIR OF PULMONARY ATRESIA WITH VENTRICULAR SEPTAL DEFECT IN CHILDREN AT E HOSPITAL
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Abstract
Background: Pulmonary atresia with ventricular septal defect (PA-VSD) is a complex congenital heart defect with abnormal and variable morphologies of pulmonary circulation. The main objective of this study was to evaluate the surgical results in pediatrical patients undergoing repair of PA-VSD. Methods: This was a retrospective review of 107 patients who were diagnosed PA-VSD between 2015 and 2019 at E Hospital. Post operative results included mortality, morbidity, complications and re-interventions in both short and long term follow- up. Results: 51 of the 107 patients (47.7%) underwent complete surgical repair with mean age was 31.5 months and mean weight was 9.7 kg. There were 5 early deaths (9.8%), all of them were classified PA-VSD type B morphology and 4/5 cases underwent single-stage repair. 71.7% survivals had pulmonary stenosis post surgery, but only 4.3% required re- operation in early stage. During follow-up time from 7 to 64 months after surgery, there was no late death; 43.5% survivals underwent reinterventions (both percutaneous or surgical techniques), mostly due to pulmonary stenosis. The Kaplan-Meier estimated rate of freedom from reintervention at 1, 2, 3, and 5 years after repair was 85%, 70%, 63% and 56%. Conclusion: Surgical repair is an effective therapy and has low- mortality rate to treat patients with PA-VSD. The high rate of pulmonary stenosis and reinterventional requirement post operation during follow-up still remain challenges.
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Keywords
Pulmonary atresia, ventricular septal defect
References
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