CLINICAL AND CYTOGENETIC OF THREE CASES WITH ISODICENTRIC Y CHROMOSOME

Thi Hong Nhung Dinh, Thuy Lan An, Thi Thanh Moc Hoang, Thi Nga Tran, Thi Lieu Le, Thi Bich Ngoc Ngo, Thi Huyen Tran, Xuan Huy Nguyen, Chi Dung Vu, Diem Ngoc Ngo

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Tóm tắt

Isodicentric Y is one of the most common structural abnormalities of the Y chromosome. It is unstable during cell division, can generate various types of cell lines. Most reported patients are chromosomal mosaics, generally including a 45,X cell line [1]. Clinical manifestations of people carrying isodicentric Y chromosomes are usually: Turner syndrome in women, infertility in men, ambiguous genitalia, gonadal disorders, short stature... We report 3 cases: 2 females and 1 patient of unknown gender with characteristics short stature and abnormal genitalia. All 3 cases have a mosaic mosaic karyotype between the two cell lines: 46, X,idic(Y) and 45,X, have been diagnosed in cytogenetic and molecular genetic techniques at the Vietnam National Children’s Hospital.

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Tài liệu tham khảo

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